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===Epidemiology=== | ===Epidemiology=== | ||
* | *Rare. | ||
*Rarely malignant | *Rarely malignant. | ||
Familial syndromes associated with paragangliomas:<ref name=Ref_EP328>{{Ref EP|328}}</ref> | |||
*[[von Hippel Lindau]]. | |||
*Hereditary paragangliomatosis. | |||
*[[Neurofibromatosis]] type 1 (von Recklinghausen disease). | |||
*[[MEN 2A]]. | |||
*[[MEN 2B]]. | |||
*Carney-Stratakis syndrome - GISTs and [[paraganglioma]].<ref>{{Cite journal | last1 = Blay | first1 = JY. | last2 = Blomqvist | first2 = C. | last3 = Bonvalot | first3 = S. | last4 = Boukovinas | first4 = I. | last5 = Casali | first5 = PG. | last6 = De Alava | first6 = E. | last7 = Dei Tos | first7 = AP. | last8 = Dirksen | first8 = U. | last9 = Duffaud | first9 = F. | title = Gastrointestinal stromal tumors: ESMO Clinical Practice Guidelines for diagnosis, treatment and follow-up. | journal = Ann Oncol | volume = 23 Suppl 7 | issue = | pages = vii49-55 | month = Oct | year = 2012 | doi = 10.1093/annonc/mds252 | PMID = 22997454 | url = http://annonc.oxfordjournals.org/content/23/suppl_7/vii49.full }}</ref> | |||
Other associations - not proven to be genetic: | |||
*[[Carney triad]]. | |||
===Clinical=== | ===Clinical=== |
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