Cystic tumour of the atrioventricular nodal region

Cystic tumour of the atrioventricular nodal region
Diagnosis in short
Cystic tumour of the atrioventricular nodal region. H&E stain.
LM	cystic spaces lined single layer of bland epithelial cells, +/-focal mononuclear inflammation, +/-psammoma bodies
LM DDx	cystic metastatic carcinoma
IHC	CEA +ve, EMA +ve
Gross	cystic tumour in region of AV node
Grossing notes	see conducting system of heart
Site	heart - see cardiac tumour
Clinical history	sudden cardiac death
Prevalence	very rare
Prognosis	good if caught in time
Treatment	excision

Cystic tumour of the atrioventricular nodal region, abbreviated CTAVNR, is a rare cardiac tumour that can lead to sudden cardiac death.

General

• Super rare.
• Usually 1-2 mm.
• May cause sudden cardiac death.

Gross

• "Bump" in the triangle of Koch.
• Cystic spaces.

Microscopic

Features:

• Cystic spaces lined with single layer of epithelial cells.
• +/-Focal mononuclear inflammation.
• +/-Psammoma bodies.

DDx:

• Cystic metastatic carcinoma.

Images

• 

  CTAVNR - very low mag. (WC)

• 

  CTAVNR - high mag. (WC)

IHC

• CEA +ve.
• EMA +ve.

See also

• Cardiac tumours.
• Cardiac arrhythmias.
• AV node.