Cystic tumour of the atrioventricular nodal region
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| Cystic tumour of the atrioventricular nodal region | |
|---|---|
| Diagnosis in short | |
 Cystic tumour of the atrioventricular nodal region. H&E stain. | |
|
| |
| LM | cystic spaces lined by single layer of bland epithelial cells, +/-focal mononuclear inflammation, +/-psammoma bodies |
| LM DDx | cystic metastatic carcinoma |
| IHC | CEA +ve, EMA +ve |
| Gross | very small cysts in region of AV node |
| Grossing notes | see conducting system of heart |
| Site | heart - see cardiac tumour |
|
| |
| Clinical history | sudden cardiac death |
| Prevalence | very rare |
| Prognosis | good if caught in time |
| Treatment | excision |
Cystic tumour of the atrioventricular nodal region, abbreviated CTAVNR, is a rare cardiac tumour that can lead to sudden cardiac death.
General
- Super rare.[1]
- Usually 1-2 mm.
- May cause sudden cardiac death.[2]
Gross
- "Bump" in the triangle of Koch.
- Cystic spaces.
Microscopic
Features:[2]
- Cystic spaces lined with single layer of epithelial cells.
- +/-Focal mononuclear inflammation.
- +/-Psammoma bodies.
DDx:
- Cystic metastatic carcinoma.
Images
CTAVNR - very low mag. (WC)
CTAVNR - high mag. (WC)
IHC
- CEA +ve.
- EMA +ve.
See also
References
- ↑ Kaminishi, Y.; Watanabe, Y.; Nakata, H.; Shimokama, T.; Jikuya, T. (Jan 2002). "Cystic tumor of the atrioventricular nodal region.". Jpn J Thorac Cardiovasc Surg 50 (1): 37-9. PMID 11855098.
- ↑ 2.0 2.1 Paniagua, JR.; Sadaba, JR.; Davidson, LA.; Munsch, CM. (Apr 2000). "Cystic tumour of the atrioventricular nodal region: report of a case successfully treated with surgery.". Heart 83 (4): E6. PMID 10722558.