Difference between revisions of "Cystic tumour of the atrioventricular nodal region"
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*Usually 1-2 mm. | *Usually 1-2 mm. | ||
*May cause [[Sudden_natural_death|sudden cardiac death]].<ref name=pmid10722558/> | *May cause [[Sudden_natural_death|sudden cardiac death]].<ref name=pmid10722558/> | ||
*Antemortem diagnosis in case reports; only four reported in literature as of 2010.<ref name=pmid19144541>{{Cite journal | last1 = Sharma | first1 = G. | last2 = Linden | first2 = MD. | last3 = Schultz | first3 = DS. | last4 = Inamdar | first4 = KV. | title = Cystic tumor of the atrioventricular node: an unexpected finding in an explanted heart. | journal = Cardiovasc Pathol | volume = 19 | issue = 3 | pages = e75-8 | month = | year = | doi = 10.1016/j.carpath.2008.10.011 | PMID = 19144541 }}</ref> | |||
==Gross== | ==Gross== | ||
Revision as of 05:05, 21 July 2016
| Cystic tumour of the atrioventricular nodal region | |
|---|---|
| Diagnosis in short | |
 Cystic tumour of the atrioventricular nodal region. H&E stain. | |
|
| |
| Synonyms | cystic tumour of the atrioventricular node |
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| |
| LM | cystic spaces lined by single layer of bland epithelial cells, +/-focal mononuclear inflammation, +/-psammoma bodies |
| LM DDx | cystic metastatic carcinoma |
| IHC | CEA +ve, EMA +ve |
| Gross | very small cysts in region of AV node |
| Grossing notes | see conducting system of heart |
| Site | heart - see cardiac tumours |
|
| |
| Clinical history | sudden cardiac death |
| Prevalence | very rare |
| Prognosis | good if caught in time |
| Treatment | excision |
Cystic tumour of the atrioventricular nodal region, abbreviated CTAVNR, is a rare cardiac tumour that can lead to sudden cardiac death.
It is also known as cystic tumour of the atrioventricular node.
Benign mesothelioma of the atrioventricular node is also used; however, these tumours are not mesotheliomas.[1]
General
- Super rare.[2]
- Usually 1-2 mm.
- May cause sudden cardiac death.[3]
- Antemortem diagnosis in case reports; only four reported in literature as of 2010.[4]
Gross
- "Bump" in the triangle of Koch.
- Cystic spaces.
Microscopic
Features:[3]
- Cystic spaces lined with single layer of epithelial cells.
- +/-Focal mononuclear inflammation.
- +/-Psammoma bodies.
DDx:
- Cystic metastatic carcinoma.
Images
CTAVNR - very low mag. (WC)
CTAVNR - high mag. (WC)
IHC
Features:[1]
See also
References
- ↑ 1.0 1.1 Evans, CA.; Suvarna, SK. (Nov 2005). "Cystic atrioventricular node tumour: not a mesothelioma.". J Clin Pathol 58 (11): 1232. PMID 16254122.
- ↑ Kaminishi, Y.; Watanabe, Y.; Nakata, H.; Shimokama, T.; Jikuya, T. (Jan 2002). "Cystic tumor of the atrioventricular nodal region.". Jpn J Thorac Cardiovasc Surg 50 (1): 37-9. PMID 11855098.
- ↑ 3.0 3.1 Paniagua, JR.; Sadaba, JR.; Davidson, LA.; Munsch, CM. (Apr 2000). "Cystic tumour of the atrioventricular nodal region: report of a case successfully treated with surgery.". Heart 83 (4): E6. PMID 10722558.
- ↑ Sharma, G.; Linden, MD.; Schultz, DS.; Inamdar, KV.. "Cystic tumor of the atrioventricular node: an unexpected finding in an explanted heart.". Cardiovasc Pathol 19 (3): e75-8. doi:10.1016/j.carpath.2008.10.011. PMID 19144541.