Difference between revisions of "Kidney tumours"

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330 bytes added ,  02:52, 2 October 2011
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**RCC = ''partial nephrectomy'', ''nephrectomy'' or ''radical nephrectomy''.
**RCC = ''partial nephrectomy'', ''nephrectomy'' or ''radical nephrectomy''.


==Hereditary RCC==
==Hereditary renal cell carcinoma==
The classics - which are ''all'' autosomal dominant:<ref name=Ref_PBoD1016>{{Ref PBoD|1016}}</ref>
The classics - which are ''all'' autosomal dominant:<ref name=Ref_PBoD1016>{{Ref PBoD|1016}}</ref>
# [[Von Hippel-Lindau syndrome]] (clear cell tumours).  
# [[Von Hippel-Lindau syndrome]] (clear cell tumours).  
# Hereditary clear cell carcinoma (VHL gene).  
# Hereditary clear cell carcinoma (VHL gene).  
# Hereditary papillary carcinoma (MET proto-oncogene mutation).
# Hereditary papillary carcinoma (MET proto-oncogene mutation).
#* PaRCC type 1.<ref name=Ref_WMSP290>{{Ref WMSP|290}}</ref>
# Hereditary leiomyomatosis and renal cell cancer:<ref name=Ref_WMSP290>{{Ref WMSP|290}}</ref>
#* PaRCC type 2.
#* Benign leiomyomas skin/uterus.
#* Uterine [[leiomyosarcoma]].
#* FH gene (fumarate hydratase).<ref name=omim136850>{{OMIM|136850}}</ref>


Others:
Others:
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