Difference between revisions of "Ependymoma"

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'''Ependymoma''' is a [[neuropathology tumour]].   
'''Ependymoma''' is a [[neuropathology tumour]].   
* ''Myxopapillary ependymoma'' is dealt with separately in the [[myxopapillary ependymoma]] article.
* ''Subependymoma'' is dealt with separately in the [[Subependymoma]] article.


==General==  
==General==  
*Called the forgotten glial tumour.
*Called the forgotten glial tumour.
*Anatomic location is essential for tumor diagnosis.


Epidemiology:<ref name=Ref_PBoD8_1334>{{Ref PBoD8|1334}}</ref>
Epidemiology:<ref name=Ref_PBoD8_1334>{{Ref PBoD8|1334}}</ref>
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*May be associated with [[neurofibromatosis type 2]].
*May be associated with [[neurofibromatosis type 2]].


There are five main ependymal tumors:<ref name=Ref_WHOCNS_74>{{Ref WHOCNS|74}}</ref>
There are currently eight main ependymal tumors:<ref name=Ref_WHOCNS_74>{{Ref WHOCNS|74}}</ref>
#Ependymoma (not otherwise specified).
#Supratentorial ependymoma, ZFTA-fusion positive
#Supratentorial ependymoma, YAP1-fusion positive
#Posterior fossa ependymoma group A
#Posterior fossa ependymoma group B
#Spinal ependymoma
#Spinal ependymoma, MYCN-amplified
#[[Myxopapillary ependymoma]]
#[[Subependymoma]]
 
 
Ependymoma(not otherwise specified).
#*Other flavours:<ref>URL: [http://emedicine.medscape.com/article/1744030-overview http://emedicine.medscape.com/article/1744030-overview]. Accessed on: 17 January 2012.</ref>
#*Other flavours:<ref>URL: [http://emedicine.medscape.com/article/1744030-overview http://emedicine.medscape.com/article/1744030-overview]. Accessed on: 17 January 2012.</ref>
#**Papillary ependymoma.
#**Papillary ependymoma.
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#*Majority of supratentorial ependymoma in children.
#*Majority of supratentorial ependymoma in children.
#Anaplastic ependymoma.
#Anaplastic ependymoma.
#[[Myxopapillary ependymoma]].
 
#*Classically at [[filum terminale]].
 
#[[Subependymoma]].
 
#*Typically seen in IVth ventricle.


The designation ''Cellular ependymoma''  is depreceated.
The designation ''Cellular ependymoma''  is depreceated.
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*Ventricular location, but also within the spinal cord.
*Ventricular location, but also within the spinal cord.
*Dissemination possible.  
*Dissemination possible.  
*[[Myxopapillary ependymoma]] classically at [[filum terminale]].
*[[Subependymoma]] typically seen in IVth ventricle.
<gallery>
<gallery>
File:AFIP405711R-EPENDYMOMA.jpg | Radiology (AFIP)
File:AFIP405711R-EPENDYMOMA.jpg | Radiology (AFIP)
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