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Difference between revisions of "Embryonal tumour with multilayered rosettes"
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Embryonal tumour with multilayered rosettes (view source)
Revision as of 09:31, 29 September 2017
, 09:31, 29 September 2017→General: +ihc
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* Extremely rare. | * Extremely rare. | ||
* ETMR historically had been termed CNS PNET. | * ETMR historically had been termed CNS PNET. | ||
* The WHO2016 CNS classification contains two groups: | |||
**Embryonal tumour with multilayered rosettes, C19MC-altered. | |||
**Embryonal tumour with multilayered rosettes, NOS. | |||
==Clinical presentation== | |||
* Usu. age <4 years. | |||
* 70% supratentorial, 30% infratentorial. | |||
* Raised intracranial pressure. | |||
==Imaging== | |||
* Usu. enhancing. | |||
* Rarely cysts, calcifications. | |||
* Widespread infiltration. | |||
==IHC== | |||
*LIN28+ve. | |||
<gallery>File:LIN28 ependymoblastoma.jpg| LIN28 positive ETMR.</gallery> | |||