Difference between revisions of "Osteofibrous dysplasia"

==General== <ref>{{Cite web  | last =  | first =  | title = http://www.smbs.buffalo.edu/ortho/tumorarticles/osteofibrousdysplasiaandadamantinoma.pdf | url = http://www.smbs.buffalo.edu/ortho/tumorarticles/osteofibrousdysplasiaandadamantinoma.pdf | publisher =  | date =  | accessdate = 18 October 2014 }}</ref>

*Rare, benign fibro-osseous lesion

*Alternate names

**Congenital osteitis fibrosa

*Location

**Cortex of the tibial diaphysis

*Pathophysiology

**May be either a clonal neoplastic lesion or a developmental dysplasia.

**May be related to adamantinoma

*Presentation

**Lower leg swelling

**Pain

**Tibial bowing

*Radiology

**Intracortical lytic lesion

**Surrounding zone of sclerosis

**Seldom progresses radiologically

*Clinical DDX

**Adamantinoma - usually older (teens-twenties), may have soft tissue extension

**Metaphyseal fibrous defect - metaphyseal location

**Fibrous dysplasia

*Prognosis

**Self limited

*Population

**Children

**First 2 decades of life

**Median 9.5 years