Difference between revisions of "Lymphangioleiomyomatosis"

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| Other      =
| Other      =
| ClinDDx    = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]]
| ClinDDx    = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]]
| Tx        = lung transplantation
| Tx        = medical therapy, lung transplantation
}}
}}
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age.  
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age.  
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Notes:
Notes:
*Considered to be a [[PEComa]].
*Considered to be a [[PEComa]].
Treatment:<ref name=pmid25478388>{{Cite journal  | last1 = Vlachostergios | first1 = PJ. | last2 = Rad | first2 = BS. | last3 = Karimi | first3 = K. | last4 = Apergis | first4 = G. | title = Angiomyolipomas, Renal Cell Carcinomas and Pulmonary Lymphangioleiomyomatosis. | journal = J Clin Diagn Res | volume = 8 | issue = 10 | pages = MJ01 | month = Oct | year = 2014 | doi = 10.7860/JCDR/2014/9733.5021 | PMID = 25478388 }}</ref>
*Bronchodilators - symptomatic treatment.
*mTOR inhibitors. (???)
*Transplantation.


===Epidemiology===
===Epidemiology===
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