Difference between revisions of "Lymphangioleiomyomatosis"

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{{ Infobox diagnosis
| Name      = {{PAGENAME}}
| Image      =
| Width      =
| Caption    =
| Synonyms  = lymphangiomyomatosis
| Micro      = spindle cells with small nuclei + larger epithelioid cells with clear cytoplasm and round nuclei, cyst formation, thick arterial walls
| Subtypes  =
| LMDDx      =
| Stains    =
| IHC        = HMB-45 +ve, ER +ve, PR +ve, SMA +ve
| EM        =
| Molecular  =
| IF        =
| Gross      =
| Grossing  =
| Site      = [[lung]] - see ''[[medical lung diseases]]''
| Assdx      =
| Syndromes  = [[tuberous sclerosis]]
| Clinicalhx = almost always women of childbearing age, recurrent pneumothorax
| Signs      =
| Symptoms  = dyspnea
| Prevalence = very rare
| Bloodwork  =
| Rads      = bullae/thin walled cysts distributed in all lung fields, lymphadenopathy
| Endoscopy  =
| Prognosis  =
| Other      =
| ClinDDx    = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]]
| Tx        = lung transplantation
}}
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age.  
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age.  


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