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Difference between revisions of "Desmoplastic small round cell tumour"
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Desmoplastic small round cell tumour (view source)
Revision as of 16:05, 27 September 2013
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{{ Infobox diagnosis | |||
| Name = {{PAGENAME}} | |||
| Image = Desmoplastic_small_round_cell_tumour_-_high_mag.jpg | |||
| Width = | |||
| Caption = DSRCT. [[H&E stain]]. | |||
| Micro = small (round) cells in nests with an undulating sharp border, road bands of paucicellular fibrous stroma | |||
| Subtypes = | |||
| LMDDx = [[Embryonal RMS]], other [[small round cell tumours]] | |||
| Stains = | |||
| IHC = AE1/AE3 +ve, desmin +ve, EMA +ve, actin -ve, WT1 (N-terminal) -ve, WT1 (C-terminal) +ve, CD57 +ve. | |||
| EM = | |||
| Molecular = t(11;22) | |||
| IF = | |||
| Gross = | |||
| Grossing = | |||
| Site = [[soft tissue lesions]] - typically retroperitoneum | |||
| Assdx = | |||
| Syndromes = | |||
| Clinicalhx = usu. young adults | |||
| Signs = | |||
| Symptoms = | |||
| Prevalence = very rare | |||
| Bloodwork = | |||
| Rads = | |||
| Endoscopy = | |||
| Prognosis = poor | |||
| Other = | |||
| ClinDDx = (metastatic) [[germ cell tumour]], [[lymphoma]] | |||
}} | |||
'''Desmoplastic small round cell tumour''', abbreviated '''DSRCT''', is a rare malignant soft tissue lesion that tends to afflict young adults. | '''Desmoplastic small round cell tumour''', abbreviated '''DSRCT''', is a rare malignant soft tissue lesion that tends to afflict young adults. | ||