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*Secondary, e.g. due to congenital heart disease (like ventricular septal defect), interstitial pulmonary fibrosis. | *Secondary, e.g. due to congenital heart disease (like ventricular septal defect), interstitial pulmonary fibrosis. | ||
==Non-secondary pulmonary hypertension== | ===Non-secondary pulmonary hypertension=== | ||
Causes:<ref name=pmid16263465>{{cite journal |author=Bush A |title=Pulmonary hypertensive diseases |journal=Paediatr Respir Rev |volume=1 |issue=4 |pages=361-7 |year=2000 |month=December |pmid=16263465 |doi=10.1053/prrv.2000.0077 |url=}}</ref> | Causes:<ref name=pmid16263465>{{cite journal |author=Bush A |title=Pulmonary hypertensive diseases |journal=Paediatr Respir Rev |volume=1 |issue=4 |pages=361-7 |year=2000 |month=December |pmid=16263465 |doi=10.1053/prrv.2000.0077 |url=}}</ref> | ||
*Primary pulmonary hypertension. | *Primary pulmonary hypertension. | ||
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*PVOD is based on case reports - it is extremely rare.<ref name=pmid3342678>{{cite journal |author=Vevaina JR, Mark EJ |title=Thoracic hemangiomatosis masquerading as interstitial lung disease |journal=Chest |volume=93 |issue=3 |pages=657-9 |year=1988 |month=March |pmid=3342678 |doi= |url=}}</ref> | *PVOD is based on case reports - it is extremely rare.<ref name=pmid3342678>{{cite journal |author=Vevaina JR, Mark EJ |title=Thoracic hemangiomatosis masquerading as interstitial lung disease |journal=Chest |volume=93 |issue=3 |pages=657-9 |year=1988 |month=March |pmid=3342678 |doi= |url=}}</ref> | ||
==Primary pulmonary hypertension== | |||
*AKA ''pulmonary plexogenic arteriopathy''.<ref name=dccpad>Lie JT, Silver MD. Diagnostic criteria of cardiovascular pathology: acquired diseases. ISBN 0-397-51630-4. PP.208-9.</ref> | *AKA ''pulmonary plexogenic arteriopathy''.<ref name=dccpad>Lie JT, Silver MD. Diagnostic criteria of cardiovascular pathology: acquired diseases. ISBN 0-397-51630-4. PP.208-9.</ref> | ||
*Like chronic pulmonary hypertension due to congenital heart disease but ''without'' the congenital heart disease.<ref name=dccpad/> | *Like chronic pulmonary hypertension due to congenital heart disease but ''without'' the congenital heart disease.<ref name=dccpad/> | ||
**Classified by ''Heath-Edwards classification'' (see below) into six grades. | **Classified by ''Heath-Edwards classification'' (see below) into six grades. | ||
==Pulmonary veno-occlusive disease (PVOD)== | |||
Features:<ref>PPP PP.393-6.</ref> | Features:<ref>PPP PP.393-6.</ref> | ||
*Clinical - gradual dyspnea +/- non-productive cough, +/- clubbing. | *Clinical - gradual dyspnea +/- non-productive cough, +/- clubbing. | ||
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DDx: chronic interstitial pneumonia. | DDx: chronic interstitial pneumonia. | ||
==Pulmonary capillary hemangiomatosis (PCH)== | |||
General: | General: | ||
*First reported in 1978 by Wagenvoort et al..<ref name=pmid730121>{{cite journal |author=Wagenvoort CA, Beetstra A, Spijker J |title=Capillary haemangiomatosis of the lungs |journal=Histopathology |volume=2 |issue=6 |pages=401-6 |year=1978 |month=November |pmid=730121 |doi= |url=}}</ref> | *First reported in 1978 by Wagenvoort et al..<ref name=pmid730121>{{cite journal |author=Wagenvoort CA, Beetstra A, Spijker J |title=Capillary haemangiomatosis of the lungs |journal=Histopathology |volume=2 |issue=6 |pages=401-6 |year=1978 |month=November |pmid=730121 |doi= |url=}}</ref> | ||
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==See also== | ==See also== | ||
*[[Medical lung diseases]]. | *[[Medical lung diseases]]. | ||
*[[Congenital heart disease]]. | |||
*[[Heart]]. | *[[Heart]]. | ||
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