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Difference between revisions of "Von Hippel-Lindau disease"
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→Pancreatic islet cell tumours: tweak
(+pancreatic neuroendocrine tumour) |
(→Pancreatic islet cell tumours: tweak) |
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*1 in 40,000 live births.<ref name=pmid11578646>{{cite journal |author=Singh AD, Shields CL, Shields JA |title=von Hippel-Lindau disease |journal=Surv Ophthalmol |volume=46 |issue=2 |pages=117–42 |year=2001 |pmid=11578646 |doi= |url=}}</ref> | *1 in 40,000 live births.<ref name=pmid11578646>{{cite journal |author=Singh AD, Shields CL, Shields JA |title=von Hippel-Lindau disease |journal=Surv Ophthalmol |volume=46 |issue=2 |pages=117–42 |year=2001 |pmid=11578646 |doi= |url=}}</ref> | ||
==Pancreatic islet cell | ==Pancreatic neuroendocrine tumour== | ||
{{Main|Pancreatic neuroendocrine tumour}} | |||
*[[AKA]] ''pancreatic islet cell tumour'' | |||
In VHL these have distinct morphology: | In VHL these have distinct morphology: | ||
*Clear cells<ref name=pmid10740008>{{Cite journal | last1 = Musso | first1 = C. | last2 = Paraf | first2 = F. | last3 = Petit | first3 = B. | last4 = Archambeaud-Mouveroux | first4 = F. | last5 = Valleix | first5 = D. | last6 = Labrousse | first6 = F. | title = [Pancreatic neuroendocrine tumors and von Hippel-Lindau disease]. | journal = Ann Pathol | volume = 20 | issue = 2 | pages = 130-3 | month = Mar | year = 2000 | doi = | PMID = 10740008 }}</ref> - unusual in [[neuroendocrine tumours]]. | *Clear cells<ref name=pmid10740008>{{Cite journal | last1 = Musso | first1 = C. | last2 = Paraf | first2 = F. | last3 = Petit | first3 = B. | last4 = Archambeaud-Mouveroux | first4 = F. | last5 = Valleix | first5 = D. | last6 = Labrousse | first6 = F. | title = [Pancreatic neuroendocrine tumors and von Hippel-Lindau disease]. | journal = Ann Pathol | volume = 20 | issue = 2 | pages = 130-3 | month = Mar | year = 2000 | doi = | PMID = 10740008 }}</ref> - unusual in [[neuroendocrine tumours]] otherwise. | ||
*Fibrosis. (???) | *Fibrosis. (???) | ||