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Difference between revisions of "Medical liver disease"
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Medical liver disease (view source)
Revision as of 03:34, 29 November 2011
, 03:34, 29 November 2011→Other: create BCS
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=Other= | =Other= | ||
==Budd-Chiari syndrome== | |||
*[[AKA]] ''hepatic vein obstruction'' | |||
===General=== | |||
*Hepatic outflow obstruction. | |||
Clinical triad:<ref name=pmid21573256>{{Cite journal | last1 = Fox | first1 = MA. | last2 = Fox | first2 = JA. | last3 = Davies | first3 = MH. | title = Budd-Chiari syndrome--a review of the diagnosis and management. | journal = Acute Med | volume = 10 | issue = 1 | pages = 5-9 | month = | year = 2011 | doi = | PMID = 21573256 }}</ref> | |||
*Ascites. | |||
*Abdominal pain. | |||
*Hepatomegaly. | |||
Etiology: | |||
*~50% have a [[myeloproliferative disorder]].<ref name=pmid18814079>{{Cite journal | last1 = Plessier | first1 = A. | last2 = Valla | first2 = DC. | title = Budd-Chiari syndrome. | journal = Semin Liver Dis | volume = 28 | issue = 3 | pages = 259-69 | month = Aug | year = 2008 | doi = 10.1055/s-0028-1085094 | PMID = 18814079 }}</ref> | |||
Clinical DDx: | |||
*[[Hepatic veno-occlusive disease]]. | |||
===Microscopic=== | |||
Features:<ref name=pmid17569137>{{Cite journal | last1 = Aydinli | first1 = M. | last2 = Bayraktar | first2 = Y. | title = Budd-Chiari syndrome: etiology, pathogenesis and diagnosis. | journal = World J Gastroenterol | volume = 13 | issue = 19 | pages = 2693-6 | month = May | year = 2007 | doi = | PMID = 17569137 | url=http://www.wjgnet.com/1007-9327/full/v13/i19/2693.htm }}</ref> | |||
*Sinusoidal dilation in zone III (congestion). | |||
*+/-Hepatocyte drop-out. | |||
*+/-Centrilobular fibrosis. | |||
DDx congestion: | |||
*Congestive heart failure ([[congestive hepatopathy]]). | |||
*Constrictive pericarditis. | |||
==Vanishing bile duct syndrome== | ==Vanishing bile duct syndrome== | ||
*[[AKA]] ''bile duct loss'', [[AKA]] ''ductopenia''.<ref name=pmid11521176/> | *[[AKA]] ''bile duct loss'', [[AKA]] ''ductopenia''.<ref name=pmid11521176/> | ||