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Difference between revisions of "Lymphangioleiomyomatosis"
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Lymphangioleiomyomatosis (view source)
Revision as of 06:02, 9 December 2014
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{{ Infobox diagnosis | |||
| Name = {{PAGENAME}} | |||
| Image = | |||
| Width = | |||
| Caption = | |||
| Synonyms = lymphangiomyomatosis | |||
| Micro = spindle cells with small nuclei + larger epithelioid cells with clear cytoplasm and round nuclei, cyst formation, thick arterial walls | |||
| Subtypes = | |||
| LMDDx = | |||
| Stains = | |||
| IHC = HMB-45 +ve, ER +ve, PR +ve, SMA +ve | |||
| EM = | |||
| Molecular = | |||
| IF = | |||
| Gross = | |||
| Grossing = | |||
| Site = [[lung]] - see ''[[medical lung diseases]]'' | |||
| Assdx = | |||
| Syndromes = [[tuberous sclerosis]] | |||
| Clinicalhx = almost always women of childbearing age, recurrent pneumothorax | |||
| Signs = | |||
| Symptoms = dyspnea | |||
| Prevalence = very rare | |||
| Bloodwork = | |||
| Rads = bullae/thin walled cysts distributed in all lung fields, lymphadenopathy | |||
| Endoscopy = | |||
| Prognosis = | |||
| Other = | |||
| ClinDDx = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]] | |||
| Tx = lung transplantation | |||
}} | |||
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age. | '''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age. | ||