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Difference between revisions of "Lymphangioleiomyomatosis"
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Lymphangioleiomyomatosis (view source)
Revision as of 06:07, 9 December 2014
, 06:07, 9 December 2014no edit summary
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| Other = | | Other = | ||
| ClinDDx = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]] | | ClinDDx = [[eosinophilic granuloma]], [[usual interstitial pneumonia]], [[emphysema]] | ||
| Tx = lung transplantation | | Tx = medical therapy, lung transplantation | ||
}} | }} | ||
'''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age. | '''Lymphangioleiomyomatosis''', abbreviated '''LAM''', is a rare [[medical lung disease|lung pathology]] that predominantly afflicits women of childbearing age. | ||
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Notes: | Notes: | ||
*Considered to be a [[PEComa]]. | *Considered to be a [[PEComa]]. | ||
Treatment:<ref name=pmid25478388>{{Cite journal | last1 = Vlachostergios | first1 = PJ. | last2 = Rad | first2 = BS. | last3 = Karimi | first3 = K. | last4 = Apergis | first4 = G. | title = Angiomyolipomas, Renal Cell Carcinomas and Pulmonary Lymphangioleiomyomatosis. | journal = J Clin Diagn Res | volume = 8 | issue = 10 | pages = MJ01 | month = Oct | year = 2014 | doi = 10.7860/JCDR/2014/9733.5021 | PMID = 25478388 }}</ref> | |||
*Bronchodilators - symptomatic treatment. | |||
*mTOR inhibitors. (???) | |||
*Transplantation. | |||
===Epidemiology=== | ===Epidemiology=== | ||