Other CNS embryonal tumours
Other CNS embryonal tumor, was introduced in the WHO 2016 classification of CNS tumors. Some of these tumors of this category has been previously designated as CNS-PNET but this terminology has been abandoned.
| Other CNS embryonal tumours | |
|---|---|
| Diagnosis in short | |
 Other CNS embryonal tumorH&E stain. | |
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| |
| Synonyms | CNS-PNET |
| LM DDx | small round blue cell tumours |
| IHC | S-100 +ve, Syn +/-ve |
| Site | brain, spinal cord |
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| |
| Prevalence | rare - typically in children and young adults |
| Prognosis | poor (WHO Grade IV) |
General
Other CNS embryonal tumours are a group of primitive neuroeptithelial tumors that are to be classified in distinct molecular groups in the future.
DDx:
- AT/RT
- ETMR
- Anaplastic ependymoma
- H3F3A G34-mutated Glioblastoma