Localized cystic disease of the kidney

Localized cystic disease of the kidney is a rare benign entity that should be separated from hereditary cystic kidney diseases and cystic renal tumours.

It is also known as segmental cystic disease of the kidney and unilateral cystic disease of the kidney.

General

• Rare.
• Benign.
• Bosniak classification 2 or 3.

Gross

Features:

• Cystic lesion without capsule.

Microscopic

Features:

• Cuboidal or flat lining epithelium - contiguous with renal collecting ducts.
• No significant inflammation.

DDx:

• Cystic renal cell carcinoma.
• Autosomal dominant polycystic kidney disease.

See also

• Cystic kidney diseases.