Tuberous sclerosis-associated renal cell carcinoma
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Tuberous sclerosis-associated renal cell carcinoma, abbreviated TSARCC, is a recently described renal tumour that is associated with the syndrome tuberous sclerosis.[1]
General
- Recently described - not in the WHO classification of renal neoplasia.
Microscopic
Features - one of three morphologies:[1]
- Renal angiomyoadenomatous tumour-like.
- Chromophobe renal cell carcinoma-like.
- Macrocystic architecture with cells with granular eosinophilic cytoplasm.
DDx:
- Renal angiomyoadenomatous tumour.
- Chromophobe renal cell carcinoma.
- Hereditary leiomyomatosis renal cell carcinoma syndrome-associated renal cell carcinoma.
See also
References
- ↑ 1.0 1.1 Guo, J.; Tretiakova, MS.; Troxell, ML.; Osunkoya, AO.; Fadare, O.; Sangoi, AR.; Shen, SS.; Lopez-Beltran, A. et al. (Nov 2014). "Tuberous Sclerosis-associated Renal Cell Carcinoma: A Clinicopathologic Study of 57 Separate Carcinomas in 18 Patients.". Am J Surg Pathol 38 (11): 1457-67. doi:10.1097/PAS.0000000000000248. PMID 25093518.