Difference between revisions of "Retroperitoneal fibrosis"

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==General==
==General==
*May cause obstructive uropathy.<ref name=pmid19668300/>
*May cause obstructive uropathy.<ref name=pmid19668300/>
*One of the many [[IgG4-related systemic disease]]s.<ref name=pmid18609677>{{Cite journal  | last1 = Kamisawa | first1 = T. | last2 = Okamoto | first2 = A. | title = IgG4-related sclerosing disease. | journal = World J Gastroenterol | volume = 14 | issue = 25 | pages = 3948-55 | month = Jul | year = 2008 | doi =  | PMID = 18609677 }}</ref>
*No standard diagnostic criteria.<ref name=pmid23597969>{{Cite journal  | last1 = Scheel | first1 = PJ. | last2 = Feeley | first2 = N. | title = Retroperitoneal fibrosis. | journal = Rheum Dis Clin North Am | volume = 39 | issue = 2 | pages = 365-81 | month = May | year = 2013 | doi = 10.1016/j.rdc.2013.02.004 | PMID = 23597969 }}</ref>


Treatment:
Treatment:<ref name=pmid23597969/>
*Immunosuppression.
*Immunosuppression.
*Ureteral stents - to avoid [[renal failure]].


==Microscopic==
==Microscopic==
Features:<ref>URL: [http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html]. Accessed on: 20 October 2011.</ref><ref name=pmid19668300>{{Cite journal  | last1 = Rodríguez Jornet | first1 = A. | last2 = Andreu Navarro | first2 = FJ. | last3 = Orellana Fernández | first3 = R. | last4 = Ibeas López | first4 = J. | last5 = García García | first5 = M. | title = [Idiopathic retroperitoneal fibrosis: clinico-pathological characteristics]. | journal = Nefrologia | volume = 29 | issue = 4 | pages = 298-303 | month =  | year = 2009 | doi = 10.3265/Nefrologia.2009.29.4.5344.en.full | PMID = 19668300 }}
Features:<ref>URL: [http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html]. Accessed on: 20 October 2011.</ref><ref name=pmid19668300>{{Cite journal  | last1 = Rodríguez Jornet | first1 = A. | last2 = Andreu Navarro | first2 = FJ. | last3 = Orellana Fernández | first3 = R. | last4 = Ibeas López | first4 = J. | last5 = García García | first5 = M. | title = [Idiopathic retroperitoneal fibrosis: clinico-pathological characteristics]. | journal = Nefrologia | volume = 29 | issue = 4 | pages = 298-303 | month =  | year = 2009 | doi = 10.3265/Nefrologia.2009.29.4.5344.en.full | PMID = 19668300 }}
</ref>
</ref>
*Fibrous tissue (pink background) with inflammatory cells like plasma cells, benign lymphocytes and eosinophils. The white open spaces are entrapped adipocytes.
*Fibrous tissue (pink background) with inflammatory cells (plasma cells, benign lymphocytes and eosinophils).  


Images:
Note:
*Entrapped adipocytes (white open spaces) are common.
 
===Images===
www:
*[http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html Retroperiteonal fibrosis (mypacs.net)].
*[http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html Retroperiteonal fibrosis (mypacs.net)].
==Sign out==
<pre>
A. KIDNEY, RIGHT, RADICAL NEPHRECTOMY:
- SEVERE PYELONEPHRITIS, CHRONIC ACTIVE.
- EXTENSIVE TOTAL SCLEROSIS OF GLOMERULI AND INTERSTITIAL FIBROSIS (END-STAGE KIDNEY).
- PERIRENAL FAT WITH FOCI OF FAT NECROSIS, FIBROSIS AND A MIXED INFLAMMATORY
  INFILTRATE WITH PLASMA CELLS.
- NEGATIVE FOR MALIGNANCY.
B. SOFT TISSUE, RETROPERITONEUM, BIOPSY:
- FIBROTIC SOFT TISSUE WITH A MINIMAL FOCAL LYMPHOCYTIC INFILTRATE.
- NEGATIVE FOR MALIGNANCY.
</pre>


==See also==
==See also==
*[[Riedel thyroiditis]].
*[[Riedel thyroiditis]].
*[[IgG4-related systemic disease]].


==References==
==References==

Latest revision as of 20:22, 30 October 2013

Retroperitoneal fibrosis is a rare thingy urologists and rheumatologists dealt with.

General

Treatment:[3]

Microscopic

Features:[4][1]

  • Fibrous tissue (pink background) with inflammatory cells (plasma cells, benign lymphocytes and eosinophils).

Note:

  • Entrapped adipocytes (white open spaces) are common.

Images

www:

Sign out

A. KIDNEY, RIGHT, RADICAL NEPHRECTOMY:
- SEVERE PYELONEPHRITIS, CHRONIC ACTIVE.
- EXTENSIVE TOTAL SCLEROSIS OF GLOMERULI AND INTERSTITIAL FIBROSIS (END-STAGE KIDNEY).
- PERIRENAL FAT WITH FOCI OF FAT NECROSIS, FIBROSIS AND A MIXED INFLAMMATORY
  INFILTRATE WITH PLASMA CELLS.
- NEGATIVE FOR MALIGNANCY.

B. SOFT TISSUE, RETROPERITONEUM, BIOPSY:
- FIBROTIC SOFT TISSUE WITH A MINIMAL FOCAL LYMPHOCYTIC INFILTRATE.
- NEGATIVE FOR MALIGNANCY.

See also

References

  1. 1.0 1.1 Rodríguez Jornet, A.; Andreu Navarro, FJ.; Orellana Fernández, R.; Ibeas López, J.; García García, M. (2009). "[Idiopathic retroperitoneal fibrosis: clinico-pathological characteristics].". Nefrologia 29 (4): 298-303. doi:10.3265/Nefrologia.2009.29.4.5344.en.full. PMID 19668300.
  2. Kamisawa, T.; Okamoto, A. (Jul 2008). "IgG4-related sclerosing disease.". World J Gastroenterol 14 (25): 3948-55. PMID 18609677.
  3. 3.0 3.1 Scheel, PJ.; Feeley, N. (May 2013). "Retroperitoneal fibrosis.". Rheum Dis Clin North Am 39 (2): 365-81. doi:10.1016/j.rdc.2013.02.004. PMID 23597969.
  4. URL: http://www.mypacs.net/cases/RETROPERITONEAL-FIBROSIS-17484372.html. Accessed on: 20 October 2011.