Difference between revisions of "Pleuropulmonary blastoma"

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(→‎General: +DICER1 syndrome)
 
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*Tumour of infancy and childhood.<ref name=pmid24101356>{{Cite journal  | last1 = Ekmekcı | first1 = S. | last2 = Aysal | first2 = A. | last3 = Olgun | first3 = N. | last4 = Olguner | first4 = M. | last5 = Cakmakci | first5 = H. | last6 = Ozer | first6 = E. | title = Pleuropulmonary Blastoma: A Case Report. | journal = Turk Patoloji Derg | volume =  | issue =  | pages =  | month = Sep | year = 2013 | doi = 10.5146/tjpath.2013.01191 | PMID = 24101356 }}</ref>  
*Tumour of infancy and childhood.<ref name=pmid24101356>{{Cite journal  | last1 = Ekmekcı | first1 = S. | last2 = Aysal | first2 = A. | last3 = Olgun | first3 = N. | last4 = Olguner | first4 = M. | last5 = Cakmakci | first5 = H. | last6 = Ozer | first6 = E. | title = Pleuropulmonary Blastoma: A Case Report. | journal = Turk Patoloji Derg | volume =  | issue =  | pages =  | month = Sep | year = 2013 | doi = 10.5146/tjpath.2013.01191 | PMID = 24101356 }}</ref>  
*May be confused radiologically with [[CCAM]].<ref name=pmid24004862>{{Cite journal  | last1 = Lezmi | first1 = G. | last2 = Verkarre | first2 = V. | last3 = Khen-Dunlop | first3 = N. | last4 = Vibhushan | first4 = S. | last5 = Hadchouel | first5 = A. | last6 = Rambaud | first6 = C. | last7 = Copin | first7 = MC. | last8 = Rittie | first8 = JL. | last9 = Benachi | first9 = A. | title = FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation. | journal = Orphanet J Rare Dis | volume = 8 | issue = 1 | pages = 130 | month = Sep | year = 2013 | doi = 10.1186/1750-1172-8-130 | PMID = 24004862 }}</ref>
*May be confused radiologically with [[CCAM]].<ref name=pmid24004862>{{Cite journal  | last1 = Lezmi | first1 = G. | last2 = Verkarre | first2 = V. | last3 = Khen-Dunlop | first3 = N. | last4 = Vibhushan | first4 = S. | last5 = Hadchouel | first5 = A. | last6 = Rambaud | first6 = C. | last7 = Copin | first7 = MC. | last8 = Rittie | first8 = JL. | last9 = Benachi | first9 = A. | title = FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation. | journal = Orphanet J Rare Dis | volume = 8 | issue = 1 | pages = 130 | month = Sep | year = 2013 | doi = 10.1186/1750-1172-8-130 | PMID = 24004862 }}</ref>
*DICER1 mutation - common, may be [[DICER1 syndrome|syndromic]].<ref name=pmid28991133>{{Cite journal  | last1 = Pierce | first1 = JM. | last2 = LaCroix | first2 = P. | last3 = Heym | first3 = K. | last4 = Bowman | first4 = WP. | last5 = Margraf | first5 = L. | last6 = Iglesias | first6 = J. | last7 = Ray | first7 = A. | title = Pleuropulmonary Blastoma: A Single-center Case Series of 6 Patients. | journal = J Pediatr Hematol Oncol | volume = 39 | issue = 8 | pages = e419-e422 | month = Nov | year = 2017 | doi = 10.1097/MPH.0000000000000972 | PMID = 28991133 }}</ref>
*[[DICER1 mutation]] - common, may be [[DICER1 syndrome|syndromic]].<ref name=pmid28991133>{{Cite journal  | last1 = Pierce | first1 = JM. | last2 = LaCroix | first2 = P. | last3 = Heym | first3 = K. | last4 = Bowman | first4 = WP. | last5 = Margraf | first5 = L. | last6 = Iglesias | first6 = J. | last7 = Ray | first7 = A. | title = Pleuropulmonary Blastoma: A Single-center Case Series of 6 Patients. | journal = J Pediatr Hematol Oncol | volume = 39 | issue = 8 | pages = e419-e422 | month = Nov | year = 2017 | doi = 10.1097/MPH.0000000000000972 | PMID = 28991133 }}</ref>


Subclassified:<ref name=pmid24041875>{{Cite journal  | last1 = Bisogno | first1 = G. | last2 = Brennan | first2 = B. | last3 = Orbach | first3 = D. | last4 = Stachowicz-Stencel | first4 = T. | last5 = Cecchetto | first5 = G. | last6 = Indolfi | first6 = P. | last7 = Bien | first7 = E. | last8 = Ferrari | first8 = A. | last9 = Dommange-Romero | first9 = F. | title = Treatment and prognostic factors in pleuropulmonary blastoma: An EXPeRT report. | journal = Eur J Cancer | volume =  | issue =  | pages =  | month = Sep | year = 2013 | doi = 10.1016/j.ejca.2013.08.015 | PMID = 24041875 }}</ref>
Subclassified:<ref name=pmid24041875>{{Cite journal  | last1 = Bisogno | first1 = G. | last2 = Brennan | first2 = B. | last3 = Orbach | first3 = D. | last4 = Stachowicz-Stencel | first4 = T. | last5 = Cecchetto | first5 = G. | last6 = Indolfi | first6 = P. | last7 = Bien | first7 = E. | last8 = Ferrari | first8 = A. | last9 = Dommange-Romero | first9 = F. | title = Treatment and prognostic factors in pleuropulmonary blastoma: An EXPeRT report. | journal = Eur J Cancer | volume =  | issue =  | pages =  | month = Sep | year = 2013 | doi = 10.1016/j.ejca.2013.08.015 | PMID = 24041875 }}</ref>

Latest revision as of 20:30, 21 August 2018

Pleuropulmonary blastoma is a very rare primary lung tumour. Traditionally, it was lumped together with well-differentiated fetal adenocarcinoma and classic biphasic pulmonary blastoma, in the category pulmonary blastoma.[1] It is now regarded a separate entity.[2]

General

Subclassified:[6]

  • Type 1.
  • Type 2.
  • Type 3.

Microscopic

Features:

DDx:

Images

www:

See also

References

  1. ↑ Walker, RI.; Suvarna, K.; Matthews, S. (May 2005). "Case report: pulmonary blastoma: presentation of two atypical cases and review of the literature.". Br J Radiol 78 (929): 437-40. doi:10.1259/bjr/45172814. PMID 15845939.
  2. ↑ Van Loo, S.; Boeykens, E.; Stappaerts, I.; Rutsaert, R. (Aug 2011). "Classic biphasic pulmonary blastoma: a case report and review of the literature.". Lung Cancer 73 (2): 127-32. doi:10.1016/j.lungcan.2011.03.018. PMID 21513998.
  3. ↑ Ekmekcı, S.; Aysal, A.; Olgun, N.; Olguner, M.; Cakmakci, H.; Ozer, E. (Sep 2013). "Pleuropulmonary Blastoma: A Case Report.". Turk Patoloji Derg. doi:10.5146/tjpath.2013.01191. PMID 24101356.
  4. ↑ Lezmi, G.; Verkarre, V.; Khen-Dunlop, N.; Vibhushan, S.; Hadchouel, A.; Rambaud, C.; Copin, MC.; Rittie, JL. et al. (Sep 2013). "FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation.". Orphanet J Rare Dis 8 (1): 130. doi:10.1186/1750-1172-8-130. PMID 24004862.
  5. ↑ Pierce, JM.; LaCroix, P.; Heym, K.; Bowman, WP.; Margraf, L.; Iglesias, J.; Ray, A. (Nov 2017). "Pleuropulmonary Blastoma: A Single-center Case Series of 6 Patients.". J Pediatr Hematol Oncol 39 (8): e419-e422. doi:10.1097/MPH.0000000000000972. PMID 28991133.
  6. ↑ Bisogno, G.; Brennan, B.; Orbach, D.; Stachowicz-Stencel, T.; Cecchetto, G.; Indolfi, P.; Bien, E.; Ferrari, A. et al. (Sep 2013). "Treatment and prognostic factors in pleuropulmonary blastoma: An EXPeRT report.". Eur J Cancer. doi:10.1016/j.ejca.2013.08.015. PMID 24041875.
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