Difference between revisions of "Neuromuscular pathology"

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*Responsive to steroids.
*Responsive to steroids.
*Enlargement of affected nerve.
*Enlargement of affected nerve.
*Variation of fiber density between fascicles / reduced axon numbers.
*CD4+ve/CD8+ve inflammatory infiltrates(approx. 65% cases).
*CD4+ve/CD8+ve inflammatory infiltrates(approx. 65% cases).
*Demyelination (thinly myelinated axons, macrophages).
*Demyelination (thinly myelinated axons, macrophages).
*Onion-bulb formations (chronic recurrent demyelination and remyelination).
*Onion-bulb formations (15-40%, chronic recurrent demyelination and remyelination).
DDx: Familial hypertrophic neuropathy.