48,460
edits
Difference between revisions of "Embryonal tumour with abundant neuropil and true rosettes"
Jump to navigation
Jump to search
Embryonal tumour with abundant neuropil and true rosettes (view source)
Revision as of 17:16, 29 September 2017
, 17:16, 29 September 2017no edit summary
(create w/ cat.) |
|||
| (3 intermediate revisions by 2 users not shown) | |||
| Line 1: | Line 1: | ||
'''Embryonal tumour with abundant neuropil and true rosettes''', abbreviated '''ETANTR''', is a very rare [[neuropathology]] tumour reported only in children. It is currently not listed in the WHO CNS tumour classification. There is consens, to group this entity together with ependymoblastomas under the umbrella term [[embryonal tumour with multilayered rosettes]] (ETMR).<ref name=pmid20532895>{{Cite journal | last1 = Paulus | first1 = W. | last2 = Kleihues | first2 = P. | title = Genetic profiling of CNS tumors extends histological classification. | journal = Acta Neuropathol | volume = 120 | issue = 2 | pages = 269-70 | month = Aug | year = 2010 | doi = 10.1007/s00401-010-0710-1 | PMID = 20532895 }}</ref> | |||
==General== | |||
*Super rare. | |||
*Reported only in children <4 years old.<ref name=pmid16551982/> | |||
* First description in 2000 by Charles Eberhart. <ref>{{Cite journal | last1 = Eberhart | first1 = CG. | last2 = Brat | first2 = DJ. | last3 = Cohen | first3 = KJ. | last4 = Burger | first4 = PC. | title = Pediatric neuroblastic brain tumors containing abundant neuropil and true rosettes. | journal = Pediatr Dev Pathol | volume = 3 | issue = 4 | pages = 346-52 | month = | year = | doi = | PMID = 10890250 }}</ref> | |||
==Microscopic== | |||
Features:<ref name=pmid20499240>{{Cite journal | last1 = Ferri Niguez | first1 = B. | last2 = Martínez-Lage | first2 = JF. | last3 = Almagro | first3 = MJ. | last4 = Fuster | first4 = JL. | last5 = Serrano | first5 = C. | last6 = Torroba | first6 = MA. | last7 = Sola | first7 = J. | title = Embryonal tumor with abundant neuropil and true rosettes (ETANTR): a new distinctive variety of pediatric PNET: a case-based update. | journal = Childs Nerv Syst | volume = 26 | issue = 8 | pages = 1003-8 | month = Aug | year = 2010 | doi = 10.1007/s00381-010-1179-x | PMID = 20499240 }}</ref> | |||
*[[Small round blue cell tumour]]. | |||
*True rosettes = flower-like cluster of cells that surrounds a space.<ref name=pmid16551982>{{cite journal |author=Wippold FJ, Perry A |title=Neuropathology for the neuroradiologist: rosettes and pseudorosettes |journal=AJNR Am J Neuroradiol |volume=27 |issue=3 |pages=488–92 |year=2006 |month=March |pmid=16551982 |doi= |url=}}</ref> | |||
*Fibrillary neuropil. | |||
**Meshwork of fibers. | |||
DDx: | |||
* CNS [[Primitive neuroectodermal tumour]]. | |||
*Desmoplastic [[Medulloblastoma]]. | |||
===Images=== | |||
*[http://path.upmc.edu/cases/case585.html ETANTR - several images (upmc.edu)]. | |||
*[http://path.upmc.edu/cases/case666.html ETANTR - another case (upmc.edu)]. | |||
==See also== | |||
*[[Neuropathology tumours]]. | |||
==References== | |||
{{Reflist|1}} | |||
[[Category:Diagnosis]] | [[Category:Diagnosis]] | ||
[[Category:Neuropathology tumours]] | |||