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Difference between revisions of "Lymphangioleiomyomatosis"
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Lymphangioleiomyomatosis (view source)
Revision as of 17:50, 10 December 2014
, 17:50, 10 December 2014→Epidemiology
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===Epidemiology=== | ===Epidemiology=== | ||
*Rare. | *Rare. | ||
*Usually affects women - primarily in childbearing years | *Usually affects women - primarily in childbearing years. | ||
**Case reports of LAM in men - usu. with [[TSC]].<ref name=pmid17431222>{{Cite journal | last1 = Schiavina | first1 = M. | last2 = Di Scioscio | first2 = V. | last3 = Contini | first3 = P. | last4 = Cavazza | first4 = A. | last5 = Fabiani | first5 = A. | last6 = Barberis | first6 = M. | last7 = Bini | first7 = A. | last8 = Altimari | first8 = A. | last9 = Cooke | first9 = RM. | title = Pulmonary lymphangioleiomyomatosis in a karyotypically normal man without tuberous sclerosis complex. | journal = Am J Respir Crit Care Med | volume = 176 | issue = 1 | pages = 96-8 | month = Jul | year = 2007 | doi = 10.1164/rccm.200610-1408CR | PMID = 17431222 }}</ref> | |||
*Associated with [[angiomyolipoma]]s. | *Associated with [[angiomyolipoma]]s. | ||
**Seen in ~30% of sporadic cases, and in ~90% of cases with tuberous sclerosis.<ref name=pmid17003820/> | **Seen in ~30% of sporadic cases, and in ~90% of cases with tuberous sclerosis.<ref name=pmid17003820/> | ||