Difference between revisions of "Chiari malformation"

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'''Chiari malformation''' is a developmental abnormality of the brain.
'''Chiari malformation''' is a developmental abnormality of the brain.


==Classification==
==General==
*Usually a radiologic diagnosis.
*May be seen in a [[fetal autopsy]].
 
===Classification===
Numbered from least severe to most severe:
Numbered from least severe to most severe:
*Chiari type I - tonsils herniated<ref>URL: [http://rarediseases.info.nih.gov/GARD/Disease.aspx?diseaseID=9230 http://rarediseases.info.nih.gov/GARD/Disease.aspx?diseaseID=9230]. Accessed on: 6 May 2011.</ref> (radiologic definition: 4-6 mm below the plane of the foramen magnum).
*Chiari type I - tonsils herniated<ref>URL: [http://rarediseases.info.nih.gov/GARD/Disease.aspx?diseaseID=9230 http://rarediseases.info.nih.gov/GARD/Disease.aspx?diseaseID=9230]. Accessed on: 6 May 2011.</ref> (radiologic definition: 4-6 mm below the plane of the foramen magnum).
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*Chiari type III - cerebellum + brain stem herniate through foramen magnum +/- encephalocele.<ref>URL: [http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm]. Accessed on: 6 May 2011.</ref>
*Chiari type III - cerebellum + brain stem herniate through foramen magnum +/- encephalocele.<ref>URL: [http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm http://www.ninds.nih.gov/disorders/chiari/detail_chiari.htm]. Accessed on: 6 May 2011.</ref>
*Chiari type IV - cerebellar hypoplasia or no cerebellum.
*Chiari type IV - cerebellar hypoplasia or no cerebellum.
==See also==
*[[Fetal autopsy]].
*[[Neuropathology]].


==References==
==References==

Revision as of 21:08, 2 January 2014

Chiari malformation is a developmental abnormality of the brain.

General

Classification

Numbered from least severe to most severe:

  • Chiari type I - tonsils herniated[1] (radiologic definition: 4-6 mm below the plane of the foramen magnum).
    • Associated with: sudden death, sleep apnea, cerebellar ataxia.
  • Chiari type II - often assoc. with hydrocephaly at birth.
  • Chiari type III - cerebellum + brain stem herniate through foramen magnum +/- encephalocele.[2]
  • Chiari type IV - cerebellar hypoplasia or no cerebellum.

See also

References