Difference between revisions of "Non-specific interstitial pneumonia"

Jump to navigation Jump to search
no edit summary
(create w/ cat.)
 
Line 1: Line 1:
#redirect [[Diffuse_lung_diseases#Non-specific_interstitial_pneumonia]]
'''Non-specific interstitial pneumonia''', abbreviated '''NSIP''', is an uncommon type of [[diffuse lung disease]].
 
==General==
*Better prognosis than [[UIP]].
*Some radiologists and pathologists don't believe in this entity.
 
Associations:<ref name=Ref_WMSP92>{{Ref WMSP|92}}</ref>
*Connective tissue disease.
*[[Rheumatoid arthritis]].
 
==Gross/Radiology==
*No honeycombing.
*Fibrosis usually lower lung zone.
*Patchy ground glass.
 
==Microscopic==
Features:<ref name=Ref_WMSP92>{{Ref WMSP|92}}</ref>
*Diffuse fibrosis:
**Uniform fibrosis (unlike [[UIP]]).
**"Linear fibrosis" has a good prognosis - should be mentioned in the report.
***''Linear fibrosis'' = fibrosis that follows alveolar walls + no architectural distortion.
*+/-Lymphoid nodules - association with collagen vascular disease. (???)
*+/-Focal [[organizing pneumonia]].
 
Notes:
*Inflammation in NSIP usually more prominent than in UIP.
*No honeycombing - key difference between UIP and NSIP.
 
DDx:
*Collagen vascular disease.
*Drug reaction.
*[[Hypersensitivity pneumonitis]] (extrinic allergic alveolitis).
*[[Lymphocytic interstitial pneumonia]] (LIP) - much more inflammation.
 
==See also==
*[[Diffuse lung diseases]].
 
==References==
{{Reflist|2}}


[[Category:Diagnosis]]
[[Category:Diagnosis]]
[[Category:Diffuse lung diseases]]
48,555

edits

Navigation menu