Difference between revisions of "Endolymphatic sac tumour"
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*Associated with [[von Hippel-Lindau disease]]. | *Associated with [[von Hippel-Lindau disease]]. | ||
Clinical - common:<ref name=pmid24436884/> | Clinical - common:<ref name=pmid24436884>{{Cite journal | last1 = Friedman | first1 = RA. | last2 = Hoa | first2 = M. | last3 = Brackmann | first3 = DE. | title = Surgical management of endolymphatic sac tumors. | journal = J Neurol Surg B Skull Base | volume = 74 | issue = 1 | pages = 12-9 | month = Feb | year = 2013 | doi = 10.1055/s-0032-1329622 | PMID = 24436884 }}</ref> | ||
*Hearing loss (sensorineural). | *Hearing loss (sensorineural). | ||
*Tinnitus. | *Tinnitus. | ||
Revision as of 17:39, 3 March 2015
Endolymphatic sac tumour, abbreviated ELST, is a very rare tumour associated with von Hippel-Lindau disease.
General
- Rare.
- Locally aggressive.[1]
- Associated with von Hippel-Lindau disease.
Clinical - common:[2]
- Hearing loss (sensorineural).
- Tinnitus.
- Dizziness.
Treatment:
- Surgical excision.[2]
Microscopic
Features:[1]
- Cystic spaces.
- Papillary structures.
- Low grade cytomorphology (lack nuclear pleomorphism).
Images
www:
IHC
- CD31 +ve - mark the outline of the papillary structures.[1]
See also
References
- ↑ 1.0 1.1 1.2 1.3 Künzel, J.; Agaimy, A.; Hornung, J.; Lell, M.; Ganslandt, O.; Semrau, S.; Zenk, J. (2014). "Sporadic endolymphatic sac tumor--a diagnostic and therapeutic challenge.". Int J Clin Exp Pathol 7 (5): 2641-6. PMID 24966979. Cite error: Invalid
<ref>tag; name "pmid24966979" defined multiple times with different content - ↑ 2.0 2.1 Friedman, RA.; Hoa, M.; Brackmann, DE. (Feb 2013). "Surgical management of endolymphatic sac tumors.". J Neurol Surg B Skull Base 74 (1): 12-9. doi:10.1055/s-0032-1329622. PMID 24436884.
- ↑ Yang, X.; Liu, XS.; Fang, Y.; Zhang, XH.; Zhang, YK. (2014). "Endolymphatic sac tumor with von Hippel-Lindau disease: report of a case with atypical pathology of endolymphatic sac tumor.". Int J Clin Exp Pathol 7 (5): 2609-14. PMID 24966975.