Difference between revisions of "Lysosomal acid lipase deficiency"

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==Microscopic==
==Microscopic==
===Liver===
Features:
Features:
*Microvesicular or mixed steatosis (microvesicular and macrovesicular).
*Microvesicular or mixed steatosis (microvesicular and macrovesicular).
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DDx:
DDx:
*[[Microvesicular steatosis]].
*[[Microvesicular steatosis]].
===Small bowel===
Features:
*Lipid accumulation - similar to [[Whipple's disease]].


==See also==
==See also==