Multicystic dysplastic kidney: Difference between revisions

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*Most common cause of abdominal mass in newborns.<ref name=emed_mrd>URL: [http://emedicine.medscape.com/article/982560-overview http://emedicine.medscape.com/article/982560-overview]. Accessed on: 4 January 2012.</ref>
*Most common cause of abdominal mass in newborns.<ref name=emed_mrd>URL: [http://emedicine.medscape.com/article/982560-overview http://emedicine.medscape.com/article/982560-overview]. Accessed on: 4 January 2012.</ref>
*May be unilateral or involve only part of a kidney.<ref name=Ref_Klatt237>{{Ref Klatt|237}}</ref>
*May be unilateral or involve only part of a kidney.<ref name=Ref_Klatt237>{{Ref Klatt|237}}</ref>
*Usually not associated with a genetic syndrome.<ref name=pmid33252759/>


Etiology: embryological malformation:<ref name=pmid33252759/>
Etiology:  
*Renal collecting system forms when ''ureteric bud'' (which grows from cloaca) meets the ''renal blastema'' (kidney parenchyma precursor).
*Embryological malformation.<ref name=pmid33252759/>
**Normal development: renal collecting system forms when ''ureteric bud'' (which grows from cloaca) meets the ''renal blastema'' (the kidney parenchyma precursor).
**In MCDK ''ureteric bud'' and ''renal blastema'' fail to meet.


==Gross==
==Gross==
*Kidney has multiple large cysts or differing sizes.
*Kidney has multiple large cysts of differing sizes.
*Normal renal pelvis is absent.<ref name=pmid33252759/>


DDx:
DDx:
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==Microscopic==
==Microscopic==
Features:<ref name=Ref_Klatt237>{{Ref Klatt|237}}</ref><ref name=pmid33252759/>
Features:<ref name=Ref_Klatt237>{{Ref Klatt|237}}</ref><ref name=pmid33252759/>
*Cystic spaces of variable size.
*Cystic spaces of variable size, lined by cuboidal cells.
*Fibrous stroma.
*Fibrous stroma.
*Islands of cartilage.
*Islands of cartilage.
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Note:
Note:
*Cysts do not communicate with one another.<ref name=pmid33252759>{{PMID| 33252759}} 33252759</ref>
*Cysts do not communicate with one another.<ref name=pmid33252759>{{cite journal |authors=Meyers ML, Treece AL, Brown BP, Vemulakonda VM |title=Imaging of fetal cystic kidney disease: multicystic dysplastic kidney versus renal cystic dysplasia |journal=Pediatr Radiol |volume=50 |issue=13 |pages=1921–1933 |date=December 2020 |pmid=33252759 |doi=10.1007/s00247-020-04755-5 |url=}}</ref>


==See also==
==See also==