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Difference between revisions of "Embryonal tumour with abundant neuropil and true rosettes"
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Embryonal tumour with abundant neuropil and true rosettes (view source)
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'''Embryonal tumour with abundant neuropil and true rosettes''', abbreviated '''ETANTR''', is a very | '''Embryonal tumour with abundant neuropil and true rosettes''', abbreviated '''ETANTR''', is a very rare [[neuropathology]] tumour reported only in children. It is currently not listed in the WHO CNS tumour classification. There is consens, to group this entity together with ependymoblastomas under the umbrella term [[embryonal tumour with multilayered rosettes]] (ETMR).<ref name=pmid20532895>{{Cite journal | last1 = Paulus | first1 = W. | last2 = Kleihues | first2 = P. | title = Genetic profiling of CNS tumors extends histological classification. | journal = Acta Neuropathol | volume = 120 | issue = 2 | pages = 269-70 | month = Aug | year = 2010 | doi = 10.1007/s00401-010-0710-1 | PMID = 20532895 }}</ref> | ||
==General== | ==General== | ||
*Super rare. | *Super rare. | ||
*Reported only in children <4 years old.<ref name=pmid16551982/> | *Reported only in children <4 years old.<ref name=pmid16551982/> | ||
* First description in 2000 by Charles Eberhart. <ref>{{Cite journal | last1 = Eberhart | first1 = CG. | last2 = Brat | first2 = DJ. | last3 = Cohen | first3 = KJ. | last4 = Burger | first4 = PC. | title = Pediatric neuroblastic brain tumors containing abundant neuropil and true rosettes. | journal = Pediatr Dev Pathol | volume = 3 | issue = 4 | pages = 346-52 | month = | year = | doi = | PMID = 10890250 }}</ref> | |||
==Microscopic== | ==Microscopic== | ||
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DDx: | DDx: | ||
*[[Primitive neuroectodermal tumour]]. | * CNS [[Primitive neuroectodermal tumour]]. | ||
*[[Medulloblastoma]]. | *Desmoplastic [[Medulloblastoma]]. | ||
===Images=== | ===Images=== | ||