Pleuropulmonary blastoma

From Libre Pathology
Jump to navigation Jump to search
The printable version is no longer supported and may have rendering errors. Please update your browser bookmarks and please use the default browser print function instead.

Pleuropulmonary blastoma is a very rare primary lung tumour. Traditionally, it was lumped together with well-differentiated fetal adenocarcinoma and classic biphasic pulmonary blastoma, in the category pulmonary blastoma.[1] It is now regarded a separate entity.[2]

General

Subclassified:[6]

  • Type 1.
  • Type 2.
  • Type 3.

Microscopic

Features:

DDx:

Images

www:

See also

References

  1. Walker, RI.; Suvarna, K.; Matthews, S. (May 2005). "Case report: pulmonary blastoma: presentation of two atypical cases and review of the literature.". Br J Radiol 78 (929): 437-40. doi:10.1259/bjr/45172814. PMID 15845939.
  2. Van Loo, S.; Boeykens, E.; Stappaerts, I.; Rutsaert, R. (Aug 2011). "Classic biphasic pulmonary blastoma: a case report and review of the literature.". Lung Cancer 73 (2): 127-32. doi:10.1016/j.lungcan.2011.03.018. PMID 21513998.
  3. Ekmekcı, S.; Aysal, A.; Olgun, N.; Olguner, M.; Cakmakci, H.; Ozer, E. (Sep 2013). "Pleuropulmonary Blastoma: A Case Report.". Turk Patoloji Derg. doi:10.5146/tjpath.2013.01191. PMID 24101356.
  4. Lezmi, G.; Verkarre, V.; Khen-Dunlop, N.; Vibhushan, S.; Hadchouel, A.; Rambaud, C.; Copin, MC.; Rittie, JL. et al. (Sep 2013). "FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation.". Orphanet J Rare Dis 8 (1): 130. doi:10.1186/1750-1172-8-130. PMID 24004862.
  5. Pierce, JM.; LaCroix, P.; Heym, K.; Bowman, WP.; Margraf, L.; Iglesias, J.; Ray, A. (Nov 2017). "Pleuropulmonary Blastoma: A Single-center Case Series of 6 Patients.". J Pediatr Hematol Oncol 39 (8): e419-e422. doi:10.1097/MPH.0000000000000972. PMID 28991133.
  6. Bisogno, G.; Brennan, B.; Orbach, D.; Stachowicz-Stencel, T.; Cecchetto, G.; Indolfi, P.; Bien, E.; Ferrari, A. et al. (Sep 2013). "Treatment and prognostic factors in pleuropulmonary blastoma: An EXPeRT report.". Eur J Cancer. doi:10.1016/j.ejca.2013.08.015. PMID 24041875.